Surgical Strategy in Partial AVSD and Mitral Cleft Repair: The Experience of a Failed Annuloplasty Ring and the Importance of ‘Ring-less’ Repair
Emre Öteyaka*, Mustafa Sedat Yıldız, Hasan Erdem, Didem Melis Öztaş, Murat Uğurlucan and Halil Türkoğlu
ABSTRACT
Mitral valve cleft is a progressive congenital anomaly that can lead to severe mitral regurgitation and pulmonary hypertension. Mitral valve cleft is often associated with complete atrioventricular canal defects. However, its association with partial defects is less common and presents unique technical challenges for surgical repair due to distorted annular geometry.
The etiology of this lesion is unknown, and diagnosis of mild cases may be difficult at an early age. Although, the severity of regurgitation and valve thickening tend to show a progressive course over time. This case report presents the clinical presentation and a critical surgical challenge treatment of a 26-year-old female patient diagnosed with mitral cleft in conjunction with a partial atrioventricular canal defect, representing an advanced example of this rare association.


















